Ehlers-Danlos syndrome ȯ¾ÆÀÇ ¸ÍÃâÀå¾Ö : Áõ·Êº¸°í
DENTAL MANAGEMENT ASSOCIATED WITH ERUPTION DISORDERS IN A PATIENT WITH EHLERS-DANLOS SYNDROME : A CASE REPORT
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±èÁ¾Ã¶ ( Kim Chong-Chul ) - ¼¿ï´ëÇб³ Ä¡ÀÇÇдëÇпø ¼Ò¾ÆÄ¡°úÇб³½Ç
ÀÌ»óÈÆ ( Lee Sang-Hoon ) - ¼¿ï´ëÇб³ Ä¡ÀÇÇдëÇпø ¼Ò¾ÆÄ¡°úÇб³½Ç
±èÁ¤¿í ( Kim Jung-Wook ) - ¼¿ï´ëÇб³ Ä¡ÀÇÇдëÇпø ¼Ò¾ÆÄ¡°úÇб³½Ç
±è¿µÀç ( Kim Young-Jae ) - ¼¿ï´ëÇб³ Ä¡ÀÇÇдëÇпø ¼Ò¾ÆÄ¡°úÇб³½Ç
ÇöÈ«±Ù ( Hyun Hong-Keun ) - ¼¿ï´ëÇб³ Ä¡ÀÇÇдëÇпø ¼Ò¾ÆÄ¡°úÇб³½Ç
½ÅÅÍÀü ( Shin Teo-Jeon ) - ¼¿ï´ëÇб³ Ä¡ÀÇÇдëÇпø ¼Ò¾ÆÄ¡°úÇб³½Ç
Àå±âÅà ( Jang Ki-Taeg ) - ¼¿ï´ëÇб³ Ä¡ÀÇÇдëÇпø ¼Ò¾ÆÄ¡°úÇб³½Ç
KMID : 1144020120080020127
Abstract
EDS´Â °üÀýÀÇ °ú¿îµ¿¼º, ÇǺÎÀÇ °ú½ÅÀå, Á¶Á÷ ¾àÈ µîÀ» ÀÓ»óÀû Ư¡À¸·Î ÇÏ´Â À¯Àü ÁúȯÀÌ´Ù. ÇǺÎ, °ñ°Ý, ±ÙÀ°, Àδë, Á¡¸·, Ç÷°ü µîÀ» ±¸¼ºÇÏ´Â ±³¿øÁúÀÇ ÇÕ¼º °úÁ¤°ú °ü·ÃµÈ À¯ÀüÀÚÀÇ °áÇÔÀ¸·Î °áÇÕÁ¶Á÷ÀÌ ºñÁ¤»óÀûÀ¸·Î º¯ÇϹǷΠ½Åü Àü¹Ý¿¡ °ÉÃÄ ±× Áõ»óÀÌ ³ªÅ¸³´Ù. ±¸° ¿µ¿ª¿¡¼µµ ±³¿ø Áú°ú °ü·ÃµÈ Á¶Á÷¿¡ ¿µÇâÀ» ¹Þ°Ô µÈ´Ù. ±¸° Á¡¸·, Ä¡ÁÖ Á¶Á÷, ÃøµÎÇϾǰüÀý ¹× Ä¡¾Æ °æÁ¶Á÷¿¡ ¹®Á¦°¡ ¹ß»ýÇÒ ¼ö ÀÖÀ¸¹Ç·Î, ÃÑüÀûÀÌ°í Á¤±âÀûÀÎ ±¸°°ü¸®°¡ ÀÌ·ç¾îÁ®¾ß ÇÑ´Ù. À̹ø Áõ·Ê¿Í °°ÀÌ EDS¿¡ ÀÇÇØ Ä¡¾ÆÀÇ ¸ÍÃâ Àå¾Ö°¡ ¹ß»ýÇÏ°í, Ä¡Àººñ´ë, À¯Âø, ¸Åº¹, ¼±ÃµÀû °á¼ÕÄ¡, ºÎÁ¤±³ÇÕ µîÀÌ °üÂûµÇ´Â °æ¿ì¿¡µµ ±¸° À§»ý °ü¸®¿Í ÇÔ²² Àå±âÀûÀÎ °èȹ ÇÏ¿¡ ¸ÍÃâ °ü¸® ¹× Ä¡·á°¡ ¿ä±¸µÈ´Ù. EDS ȯ¾ÆÀÇ Ä¡°ú Ä¡·á½Ã¿¡´Â ÁúȯÀÇ ¿øÀΰú Àü½ÅÀû Ư¡¿¡ ´ëÇÑ ÀÌÇظ¦ ¹ÙÅÁÀ¸·Î, ºñÁ¤»óÀû ±³¿øÁú ´ë»ç¿¡ ÀÇÇØ ¾àÈµÈ Á¡¸·°ú Ä¡ÁÖÁ¶Á÷, ÁöÇ÷ °ü¸®, ¹ÝÈç Çü¼º ¹× ÃøµÎÇϾǰüÀý¿¡ ´ëÇÑ Á¾ÇÕÀûÀÎ °í·Á¿Í Áö¼ÓÀûÀÎ °ü¸®°¡ ÇÊ¿äÇÏ´Ù.
Ehlers-Danlos syndrome (EDS), an inherited connective tissue disorder, is caused by mutations in genes encoding different types of collagen or collagen-processing enzymes. EDS most typically affects the joints, ligaments, skin, and blood vessels. Oral health may be severely compromised in EDS as a result of specific alterations of collagen in orofacial structures. Dental hard tissue defects, root dilaceration, pulp stones, ectopic or delayed eruption, impaction, and periodontal disease could be observed. Therefore, a number of tissue responses related to collagen and precautions should be anticipated when considering dental treatment in EDS. Long-term and comprehensive dental management is required. The purpose of this report is to describe a clinical case of eruption disorders in a patient with EDS.
Å°¿öµå
Ehlers-Danlos syndrome; Collagen; Impaction; Eruption disorder
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